To present two pediatric cases where
multifocal electroretinogram (mfERG) was able to
establish an earlier diagnosis compared to full field
electroretinogram (ERG) Case 1: an 11-year-old boy
with reduced visual acuity, pale discs, macular
pigmentation with white dots bilaterally. Case 2: a
12-year-old girl with reduced vision in her right eye,
slight pallor of the right optic disc, intense pigmentation
at both maculae and scattered punctate lesions
throughout the peripheral fundi. Both had been
investigated with electrodiagnostic tests according to
the International Society of Clinical Electrophysiology
for Vision protocol. Full-field ERGs for both
children showed normal responses. Case 1: mfERG
revealed a severe reduction in function in the inner
20. Case 2: mfERG showed attenuated responses in
each eye. Clinical examination and mfERG were
consistent with Stargardt disease. mfERG is applicable
to children and is a sensitive tool for early
diagnosis of retinal dystrophies.